A rare urogenital malformation “Herlyn-Werner-Wunderlich syndrome” (Ohvira syndrome) discovered during an acute pelvic pain

The Herlyn-Werner-Wunderlich syndrome (OHVIRA syndrome) is a rare urogenital malformation, characterized by blind hemivagina, didelphic uterus, and homolateral renal agenesis, it results from defect in the development of muller Wolf ducts during embryonic period, unknown origin, diagnosis most often made at puberty first menstruation, sometimes late, particularly for non-obstructive forms: infertility or obstetrical complications, based on pelvic ultrasound especially with 3D reconstructions magnetic resonance imaging (MRI) which remains standard gold detection mullerian anomalies, laparoscopy can also play double diagnostic prognostic role order to study consequences blood reflection (hematosalpinx, inflammatory pelvis, endometriosis. In this work we report case an OHVIRA diagnosed late age 36 years multiparous woman acute pain simulating picture torsion adnexa, will discuss through clinical, therapeutic aspects uterine malformation.